Pial arteriovenous fistula in the posterior fossa.

Furthermore high vascular lesions may present high perfusion as well as brain cancer. The symmetrical calcifications and the diffuse enhancing nodular lesions are other important findings that suggest a diffuse cerebral condition. Actually the nodular enhancing lesions constitute pre-cystic lesions as same cases show in the literature. Actually the leucodistrophy described in this entity is rather related to vasogenic edema and gliosis surrounding the cysts and the nodules. LCC is a very rare disease and less than 30 cases reported since the original description by Labrune and colleagues, all of them with characteristically infantile or juvenile onset .Sener et al. were the first to suggest the existence of an adult form of this disease, based on the observation of a slow clinical progression in a patient with onset in late adolescence. Wargon et al. report a 30-year-old woman with a lacunar infarct as the first manifestation of LCC. In our patient, the diagnosis of LCC was based on the highly suggestive neuroradiological findings which were almost identical to previous report . Our biopsy showed no neoplastic cells, but clotted blood within the lesion. LCC is an entity can present with cystic expansive lesions with mass effect, hemorrhagic content and high vascular density that can be misunderstood as neoplastic lesions. Symmetrical brain calcifications and diffuse enhancing hemorrhagic nodules are the other crucial findings. These abnormalities points out that this enity should rather be descrided as a vascular entity in the books than as a primary leucodistrophy.